Malformasi Anorektal. ANGKA KEBERHASILAN POSTEROSAGITTAL ANORECTOPLASTY (PSARP) YANG DINILAI DARI SKOR KLOTZ PADA PASIEN MALFORMASI ANOREKTAL. Faktor Risiko yang Memengaruhi Luaran Klinis Malformasi Anorektal pada Neonatus di RSUD Dr. Zainoel Abidin, Banda Aceh. Article. Full-text available.

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The injection is continued until the child voids, anorektl pictures are taken during micturition malofrmasi order to show, in a single picture, the sacrum, height of the rectum, perineum, fistula location, bladder, vesicoureteral reflux if present, and urethra.

When evaluating the results of the treatment of anorectal defects, we feel that one malformas group patients according to the traditional nomenclature into “high,” “intermediate,” and “low” defects, as malformations classified in a same group can have different treatments and different prognoses. The surgical approach to repairing these defects changed dramatically in with the introduction of the posterior sagittal approach, which allowed surgeons to view the anatomy of these defects clearly, to repair them under direct vision, and to learn about the complex anatomic arrangement of the junction of rectum and genitourinary tract.

The antegrade continence enema procedure: If catherization is not performed, overflow incontinence occurs.

The rectum and posterior vagina share a common wall, and it is this separation that is the most difficult part of the operation. The decisions involved in managing the female newborn are less complicated.

Megarectum is more common in patients for whom a transverse or loop colostomy was performed in the newborn period. Orphanet J Rare Dis. If the air column is greater than 1 cm from the perineum, a colostomy is indicated. Episodes of soiling are usually related xnorektal constipation, and when constipation is treated properly, the soiling frequently disappears.

Anorectal Malformations in Children. This sensation seems to be a consequence of stretching of the voluntary muscle proprioception.

In the case of persistent cloaca, a distended vagina hydrocolpos can be identified. The contrast material usually fills the proximal urethra and bladder through the fistula. Voluntary muscles can be used only when the patient has the sensation that it is necessary to use them.

Or, perhaps it is the hypomotility that causes dilatation, which in turn results in constipation, creating a vicious cycle. Consequently, the traditional classification of “high”, “intermediate”, and “low” defects renders the results dubious. In cases when the rectum or the vagina are very high and an abdominal approach as well is needed, laparoscopy can be used in combination with the posterior sagittal approach.


Anal canal Exquisite sensation in normal individuals resides in the anal canal. Furthermore, patients may have other spinal anomalies besides tethered cord such as syringomyelia and myelomeningocele. In a normal individual, the rectosigmoid remains quiet for variable periods of time one to several daysdepending on specific defecation habits.

Anorectal malformations

To avoid this, the distal stoma must be made intentionally small, as it will be used only for irrigations and radiologic studies. Anorectal malformations ARM represent a spectrum of abnormalities ranging from mild anal anomalies to complex cloacal malformations. For example, a one-year-old child who has undergone a pull-through for imperforate anus and has one to three bowel movements per day with no soiling in between has a great potential for future fecal continence. The repair of persistent cloacas represents a serious technical challenge that should be performed in specialized centers by pediatric surgeons dedicated to the care of these complicated patients [ 22 ].

Gynecologic concerns in the treatment of teenagers with cloaca. Surgical management of cloacal malformations: The main clinical manifestation of this is constipation, which seems to be more severe in patients with lower defects.

Both the urinary tract and the distended vagina may need to be dealt with in the newborn period to avoid serious complications. Bowel management for fecal incontinence in patients with anorectal malformations. Prognostic factors include the quality of the sacrum, the quality of the muscles, and the length of the common channel.

Complications of posterior sagittal anorectoplasty. The precise gynecologic anatomy must be ascertained either during the main malformwsi or during colostomy closure if a laparotomy was not required during the main repair. And second, should the infant undergo a primary procedure and no protective colostomy or a protective colostomy and a definitive repair at a later date?

Missing the diagnosis of cloaca frequently means that an obstructive uropathy is overlooked. These complications may compromise the ultimate functional prognosis.

Classification of anorectal malformations — initial approach, diagnostic tests, and colostomy. Presentations of pelvic pain or amenorrhea as teenagers should prompt the assumption of anomalous gynecologic structures. In males, the perineum may exhibit other features that help in recognition of this defect, such as a prominent midline skin bridge known as ‘bucket handle’ or a subepithelial midline raphe fistula that looks like a black ribbon because it is full of meconium. Clinical presentation Classification Comparing the results of reported series has always been a problem with anorectal malformations because different surgeons use different terminology when referring to types of imperforate anus.


This prevents formation of a megasigmoid, which may be responsible for the future development of constipation. The anorectal defect of imperforate anus without fistula may also be demonstrated with this radiologic evaluation. An abdominal ultrasound determines the presence of an obstructive uropathy as well as the presence of a hydrocolpos.

Anorectal malformations

Hydrostatic pressure under fluoroscopic control is required. A cross-table lateral x-ray should be performed, and will help determine the need aralah a colostomy. Anoreektal hydrostatic pressure must be high enough manual syringe injection to overcome the muscle tone of the striated muscle mechanism that surrounds the rectum and keeps it collapsed.

A simple anoplasty enlarges the stenotic orifice and relocates the rectal orifice posteriorly within the limits of the sphincter complex.

The most delicate part of this operation is the separation of the rectum and vagina, kalformasi share a common wall. In patients with imperforate anus without fistula, the same meticulous dissection is required to separate the distal rectum from the urinary tract as in patient with rectourinary fistulae because the rectum and urethra still share a common wall.

The proximal stoma is connected to the upper gastrointestinal tract and drains stool. But it should be noticed that this approach might damage the vesical nerve plexus when adalqh rectourethralfistula is dissected up to its junction with the urethra. The radiologic evaluation of a newborn with imperforate anus includes an abdominal ultrasound to evaluate for ajorektal anomalies.

All patients must be evaluated at birth to rule out one of these defects, and the most valuable screening test is an abdominal and pelvic ultrasound.

Therefore, the decision of whether to perform a colostomy or an anoplasty must wait for these 16—24 hours while the surgeon observes for clinical evidence of the baby’s anorketal anomaly. It is also the most important problem to avoid after definitive repair for female patients with rectovestibular or rectoperineal fistula and for male patients with rectobulbarurethral fistula, imperforate anus without fistula, and rectoperineal fistula.